Polyostotic fibrous displasia
Abstract
Introduction: Fibrous dysplasia is a skeletal disease characterized by the replacement of normal bone by fibrous bone tissue. The disease can most commonly affect any bones in the skull and face.
Objective: To present an 8-year-old patient who was offered the surgical modality as therapy due to polyostotic fibrous dysplasia with morphological-functional and aesthetic disorders.
Case report: A white male patient, 8 years old, came to the clinic due to nasal obstruction, increased volume of the nasolabial region, and pain in the right upper hemiarch. On physical examination, medial displacement of the lateral wall of the right nostril, deformity of the inferior turbinate, and occlusion of the nostril was observed. In oropharyngoscopy: mixed block dentition of the upper right hemiarch, increased volume of the vestibule, up to the occlusal surfaces of the teeth. Facial asymmetry with increased volume of stony consistency and pain in the right hemifacial region. On intraoral examination, mixed dentition, with blocky mobility of the upper right hemiarch, and increased volume in the vestibule to the occlusal surfaces of the teeth. Imaging studies showed a mixed lytic and sclerotic area, in ground glass, in the right upper maxillary hemiarch, maxillary sinus, orbital floor, pterygopalatine fossa and nasal septum. Considering the compressive, cosmetic, and functional oculonasosinusal manifestations, surgical treatment was performed using a Weber Ferguson incision, to expose the lower anterior, internal and orbital wall of the upper jaw.
Conclusions: Fibrous dysplasia can affect any bone in the body. Many patients have symptoms due to deformity and displacement of structures adjacent to the injuries. The indicated surgery can correct deformities, eliminate symptoms and functional and aesthetic alterations.
DeCS: FIBROUS DYSPLASIA, POLYOSTOTIC/diagnosis; FIBROUS DYSPLASIA, POLYOSTOTIC/surgery; CHILD; NASAL OBSTRUCTION; CRANIOFACIAL FIBROUS DYSPLASIA.
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22 julio 2025